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Management of Primary Pulmonary Artery Sarcoma: Experience of a Single CenterDepartment of Cardiology, Hospital Virgen de la Salud, Toledo
Department of Cardiology, Hospital Virgen de la Salud, Toledo, Departments of Cardiac Surgery, Hospital Universitario "12 de octubre," Madrid, Spain, pilar.escribano{at}telefonica.net
Departments of Cardiac Surgery, Hospital Universitario "12 de octubre," Madrid, Spain
Departments of Cardiac Surgery, Hospital Universitario "12 de octubre," Madrid, Spain
Departments of Cardiac Surgery, Hospital Universitario "12 de octubre," Madrid, Spain
Pathology, Hospital Universitario "12 de octubre," Madrid, Spain
Pathology, Hospital Universitario "12 de octubre," Madrid, Spain
Pathology (FLR, JDJ, CSC), Hospital Universitario "12 de octubre," Madrid, Spain Primary sarcoma of the pulmonary artery (PSPA) is extremely rare. Many cases are misdiagnosed as pulmonary arterial hypertension (PAH) because of chronic thromboembolic disease (CTD). Four cases of PSPA with the initial misdiagnosis are reported. The presence of a unique mass in the main pulmonary artery or proximal branches, rapidly progressive dyspnea, and constitutional symptoms should raise the suspicion of PSPA. The pathological diagnosis is usually confirmed during surgery, which is done along with adjuvant chemotherapy, the treatment of choice.
Key Words: primary sarcoma of the pulmonary artery pulmonary hypertension pulmonary thromboembolic disease diagnosis treatment
This version was published on October
1, 2008 Angiology, Vol. 59, No. 5,
636-639 (2008) |
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