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Takayasu's Arteritis Concurrent with Marfan Syndrome

A Case Report

Ki Chul Shin, MD

Yun Jong Lee, MD

Seong Wook Kang, MD

Eun Bong Lee, MD

Yeong Wook Song, MD

Department of Internal Medicine Seoul National University College of Medicine 28 Yungun-dong, Chongno-gu Seoul, 110-744, Korea

Marfan syndrome (MS) is a dominantly inherited connective tissue disorder characterized by arachnodactyly, tall stature, the presence of aortic aneurysm, and lens dislocation. Takayasu's arteritis (TA) is a chronic vasculitis that primarily affects the aorta and its branches. The authors report the first case of TA in a patient with MS. The simultaneous presence of TA and MS could be a coincidence, however; the pathogenesis of TA might be linked with autoimmunity induced by abnormal extracellular matrix protein derived from the genetic mutations in MS.

Angiology, Vol. 51, No. 5, 435-439 (2000)
DOI: 10.1177/000331970005100512


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