This Article Full Text (PDF) References Alert me when this article is cited Alert me if a correction is posted Services Email this article to a friend Similar articles in this journal Similar articles in PubMed Alert me to new issues of the journal Add to Saved Citations Download to citation manager Request Permissions Request Reprints Add to My Marked Citations Citing Articles Citing Articles via HighWire Citing Articles via Google Scholar Citing Articles via Scopus Google Scholar Articles by Rowe, J. W. Articles by Caralis, D. G. Search for Related Content PubMed PubMed Citation Articles by Rowe, J. W. Articles by Caralis, D. G. Social Bookmarking                         What's this?

Accelerated Atrioventricular Conduction in Fabry's Disease: A Case Report

Division of Clinical Physiology, Gerontology Research Center, National Institute of Child Health and Human Development, National Institutes of Health, and the Johns Hopkins University School of Medicine, Baltimore, Maryland

Dennis G. Caralis

Division of Clinical Physiology, Gerontology Research Center, National Institute of Child Health and Human Development, National Institutes of Health, and the Johns Hopkins University School of Medicine, Baltimore, Maryland

Three unrelated men with Fabry's disease (angiokeratoma corporis diffu sum universale) and accelerated atrioventricular conduction are described. AQn His bundle electrogram in one patient who reported episodes of tachycardia demonstrated a prolonged deflection preceding the ventricular complex. This deflection is thought to represent an abnormal His bundle potential, possible resulting from glycolpid deposition. In the second patient the PR interval decreased from 0.18 to 0.11 second during 10 years, and in the third patient it decreased from 0.12 to 0.10 seconds during 13 years. Accelerated atrioventricu lar conduction may develop in Fabry's disease.

Angiology, Vol. 29, No. 7, 562-568 (1978)
DOI: 10.1177/000331977802900709


CiteULike    Complore    Connotea    Del.icio.us    Digg    Reddit    Technorati    Twitter    What's this?

This article has been cited by other articles:

				J. T.R. Clarke Narrative Review: Fabry Disease Ann Intern Med, March 20, 2007; 146(6): 425 - 433. [Abstract] [Full Text] [PDF]

				M. Jastrzebski, B. Bacior, P. P. Dimitrow, and K. Kawecka-Jaszcz Electrophysiological study in a patient with Fabry disease and a short PQ interval Europace, December 1, 2006; 8(12): 1045 - 1047. [Abstract] [Full Text] [PDF]